While bicuspid aortic valve (BAV) is the most common congenital cardiac anomaly, quadricuspid aortic valve (QAV) is a rare entity. The usual three-leaflet aortic valve is characterized by engineering advantages with superior long term performance and thus degenerative changes and significant functional deterioration appear at advanced age.
Aim: Evaluation of long term performance, similarities and differences between QAV and BAV. Methods: Screening of 19000 consecutive echocardiographic studies was performed.
Results: BAV was reported in 131subjects with a prevalence of 0.7% while QAV was seen in 11with a prevalence of 0.06%, P
Conclusions: BAV is a common congenital anomaly while QAV is rare. Similar prevalence of significant valve disease and aortopathy is encountered in both anomalies, though at younger age in BAV patients.