Brugada Syndrome — A Case Report

Introduction: Brugada syndrome is a type of arrhythmia disorder, it is the major cause of sudden death in adults and the most common reason for unexplained death without known underlying cardiac disease.

The syndrome is mostly genetic disorder frequently causes cardiac death due to ventricular fibrillation. The most frequent sign is a persistent ST elevation in the electrocardiographic leads V1-V3 with a right bundle branch block (RBBB).

Case Report: A healthy 12-year-old girl that was admitted to the Emergency Department due to syncope at midnight, Familiar anamnesis was negative.

In the ambulance, ECG showed VT that responded to the treatment by Procor IV.

In the emergency department, the ECG showed a Picture of Brugada Syndrome.

Physical examination showed stable vital signs. The laboratory tests showed normal values of magnesium; Troponin and CPK were normal.

A chest x-ray was normal, Echocardiogram without evidence of myocarditis or cardiomyopathy.

The child was sent to the ICU and treated with Procor and β-blockers.

Followed by electrophysiological evaluation for ICD transplantation.

Discussion: Three different types of ECG patterns in Brugada syndrome are known.

Signs and symptoms:

• Syncope and/or cardiac arrest: occurs during sleep at night or at rest.
• Nightmares at night.
• Asymptomatic.

Treatment may include application of an ICD. β-blockers and Quinidine are effective for patients with unstable ventricular arrhythmias.

Concllusion: Brugada syndrome is a very rare arrhythmia disorder. The physicians must think of it when repeated syncope and/or nightmare were found in healthy children and try to find the typical ECG findings.