Congenital Intrahepatic Portosystemic Shunt In Neonate

Introduction: portosystemic shunt , also known as a liver shunt, is a bypass of the liver by the body`s circulatory system. It can be either a congenital or acquired condition. Congenital portosystemic venous shunts (CPSVS) are rare vascular anomalies that occur secondary to abnormal development or involution of fetal vasculature. CPSVS can be divided into two types: intrahepatic shunts and less commonly the extrahepatic type. CPSVS are associated with multiple congenital abnormalities.

Case Report: A full-term newborn baby female was born by caesarean section due to fetal bradycardia. Normal physical examination except for the impression of slightly short limbs, frontal boosing, and Hepatosplenomegaly. In light of cholestatic jaundice with high levels of direct bilirubin, Ursolit treatment was applied, on abdominal ultrasound Portosystemic hepatic shunt was detected, and a communication was demonstrated with curling and dilation of the hepatic vein and its small branches with mixed flow of the two veins attachment at two points. normal ammonia and normal coagulation functions was detected. A shunt has been demonstrated that shows a connection in the middle branch of the hepatic vein and the portal vein. brain ultrasound was normal. At the age of six months the child was asymptomatic and stable, a repeat ultrasound detected improvement and showed minimal shunt between the portal vein and the hepatic vein, and was in the closing process.

Conclusion: the diagnosis of the portosystemic shunts is often challenging and requires a high degree of clinical suspicion. Spontaneous closure of CPSS can occur in some anatomic forms during the first year of life. Upon discovery of a CPSS in a child, it is important to rule out portal hypertension.